Cat#:PA-3925F;Product Name:Mouse Anti-ATPase p97 Antibody;Synonym:15S Mg(2+) ATPase p97 subunit; 15S Mg(2+)-ATPase p97 subunit; ATPase p97; IBMPFD; MGC131997; MGC148092; MGC8560; p97; TER ATPase; TERA; TERA_HUMAN; transitional endoplasmic reticulum ATPase; Valosin containing protein; valosin-containing protein; VCP; yeast Cdc48p homolog; ATPase; Adenosine Triphosphatase;Background:Defects in VCP are the cause of inclusion body myopathy with early-onset Paget disease and frontotemporal dementia (IBMPFD) [MIM:167320]; also known as muscular dystrophy, limb-girdle, with Paget disease of bone or pagetoid amyotrophic lateral sclerosis or pagetoid neuroskeletal syndrome or lower motor neuron degeneration with Paget-like bone disease. IBMPFD features adult-onset proximal and distal muscle weakness (clinically resembling limb girdle muscular dystrophy), early-onset Paget disease of bone in most cases and premature frontotemporal dementia.;Description:Mouse Anti-ATPase p97 Monoclonal Antibody;Host Species:Mouse;Species Reactivity:Human;Clone#:58.13.4;Isotype:IgG1;Application:WB;Storage:Store antibody products at 2-8°C. For long term storage, aliquot and freeze at -20°C. Avoid repeated freeze/thaw cycles;Usage:For Lab Research Use Only;